Unilateral agenesis of lung associated with total anomalous pulmonary venous return and atrial septal defect

Pavlović Vesna 1 , Stojanović Vesna 1 , Doronjski Aleksandra 1 , Kovačević Branka 1 , and Adjić Oto 2
  • 1 Institute for Child and Youth Health Care of Vojvodina, Intensive Unit Care, Hajduk Veljkova 10, 21000, Novi Sad, Serbia
  • 2 Institute of Nuclear Medicine, Institutski put 4, 21204, Sremska Kamenica, Serbia


Presented, is the case of a newborn with left-sided lung agenesis associated with total anomalous pulmonary venous return, atrial septal defect, polysplenia and hypospadias was described. Throughout the entire hospitalization period the newborn was in poor general condition, and dependent on mechanical ventilation with high oxygen concentrations. On day 20, the newborn died. According to the available literature, this case is unique in regard to the type and number of malformations.

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